Introducción. “Esclerodermia” significa “piel dura”. El término. “esclerodermia localizada” como diagnóstico principal se refiere al hecho de que las. vol número4 Aplicación del Examen Clínico Objetivo Estructurado en la residencia de Pediatría de la Ciudad de Buenos Angiomas venosos y cefalea en . Morfea o esclerodermia localizada juvenil, descripción de caso clínico y actualización. 9. Arkachaisri T, Vilaiyuk S, Li S, O’Neill KM, Pope E, Higgins.
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In juvenile localized scleroderma JLSnew techniques such as Doppler and laser Doppler imaging have shown their usefulness for the daily monitoring of the patients.
We report a case of linear and pansclerotic ELJ type, in which there was a 2 year delay in diagnosis, however the response to treatment was positive as expected. Morphea or juvenile localised scleroderma: To report a case of Pediatrja Localised scleroderma in an 8-year old girl, contributing to an early diagnosis and treatment.
Morfea o esclerodermia localizada juvenil: caso clínico
She started with immunosuppressive therapy, physiotherapy, and occupational therapy. Recent studies, concerning histopathology and clinical associations with other conditions, open new horizons on the etiopathogenesis of scleroderma. Morphea; Juvenile localised scleroderma; Pediatriq.
Esclerodermis clinical features and diagnostic tests, including histology were compatible with linear and pansclerotic JLS. The case is presented of an 8 year-old girl who presented with indurated hypopigmented plaques, of linear distribution in the right upper extremity of two years onset, together with papery texture hyperpigmented indurated plaques with whitish areas of thinned skin in right lower extremity, and leg and ankle swelling.
In juvenile systemic sclerosis JSSca new severity score has been developed and needs to be validated in future trials. New developments have been also reached in the field of outcome measures.
Scleroderma in children: an update.
Finally, a randomized, double-blind controlled trial, a multicenter consensus statement and long-term follow-up studies have confirmed the important role of methotrexate MTX for the treatment of JLS. Morphea or juvenile localised pediateia JLS is an autoimmune, inflammatory, chronic, slowly progressive connective tissue disease of unknown cause that preferably affects skin and underlying tissues. Scleroderma, in its localized and systemic presentation, represents the pediatrria most frequent rheumatic condition in childhood after juvenile idiopathic arthritis and systemic lupus erythematosus.
Studies over recent years highlighted the role of imaging as outcome measures for JLS and introduced a severity score for JSSc. Early diagnosis, appropriate assessment and effective treatment are crucial to improve the long-term outcome.